Pregled bibliografske jedinice broj: 734784
Combined auxiliary split liver and kidney transplantation for type I primary hyperoxaluria and end-stage kidney disease
Combined auxiliary split liver and kidney transplantation for type I primary hyperoxaluria and end-stage kidney disease // Nephrology, 19 (2014), 12; 814-815 doi:10.1111/nep.12325 (međunarodna recenzija, pismo, znanstveni)
CROSBI ID: 734784 Za ispravke kontaktirajte CROSBI podršku putem web obrasca
Naslov
Combined auxiliary split liver and kidney
transplantation for type I primary hyperoxaluria
and end-stage kidney disease
Autori
Knotek, Mladen ; Maksimović, Bojana ; Gunjača, Mihaela ; Mihovilović, Karlo ; Galešić Ljubanović, Danica ; Kocman, Branislav
Izvornik
Nephrology (1320-5358) 19
(2014), 12;
814-815
Vrsta, podvrsta i kategorija rada
Radovi u časopisima, pismo, znanstveni
Ključne riječi
liver and kidney transplantation ; type I primary hyperoxaluria ; end-stage kidney disease
Sažetak
Primary hyperoxaluria type 1 (PH1) is a rare autosomal recessive disease, caused by loss of function in liver-specific alanine-glyoxylate aminotransferase (AGT). Accumulation of oxalate in PH1 causes nephrocalcinosis and urolithiasis leading to end-stage kidney (ESKD) in 90% of patients.1 These patients are treated by combined liver and kidney transplantation (LKT). Liver transplantation (LT) in PH1 has traditionally been performed as an orthotopic whole LT.2 Combined auxiliary LKT may mitigate the risk of whole LT, because native liver is preserved.
Izvorni jezik
Engleski
Znanstvena područja
Kliničke medicinske znanosti
POVEZANOST RADA
Projekti:
MZOS-044-0000000-3356 - Imunološki nadzor u bolesnika s transplantiranim solidnim organom (Knotek, Mladen, MZOS ) ( CroRIS)
MZOS-198-0000000-3355 - Značaj morfoloških čimbenika u dijagnostici, terapiji i prognozi FSGS (Galešić-Ljubanović, Danica, MZOS ) ( CroRIS)
Ustanove:
Klinička bolnica "Merkur",
Medicinski fakultet, Zagreb,
Klinička bolnica "Dubrava"
Citiraj ovu publikaciju:
Časopis indeksira:
- Current Contents Connect (CCC)
- Web of Science Core Collection (WoSCC)
- Science Citation Index Expanded (SCI-EXP)
- SCI-EXP, SSCI i/ili A&HCI
- Scopus
- MEDLINE