Naslov
Systemic sclerosis-associated pulmonary disorders

Autori
Peroš-Golubičić, Tatjana:Samaržija, Miroslav

Vrsta, podvrsta i kategorija rada
Poglavlja u knjigama, stručni

Knjiga
Lung in non-pulmonary and systemic disease

Urednik/ci
Peroš-Golubičić, Tatjana

Izdavač
Medicinska naklada

Grad
Zagreb

Godina
2013

Raspon stranica
261-277

ISBN
978-953-176-577-0

Ključne riječi
Sytemic sclerosis, pulmonary manifestations

Sažetak
Systemic sclerosis is a chronic, progressive multiorgan disease in which considerable fibrosis, vascular alterations, and autoantibodies against diverse antigens are among the principal features. The disease is of unknown cause. Most frequent extracutaneous involvement is the lung. Interstitial lung disease and pulmonary hypertension are the most common clinical expressions of lung involvement and most serious events concerning the prognosis. Clinically significant interstitial lung disease in patients with systemic sclerosis is observed in about 40% of cases, varying from 19% to 47. The rate of pulmonary hypertension varies between 8% and 32% in different studies. The prognosis of patients with systemic sclerosis today in most instances depends upon pulmonary complications. The systemic sclerosis associated interstitial lung disease and pulmonary hypertension will be described and their current and future therapies presented.

Izvorni jezik
Engleski

Znanstvena područja
Kliničke medicinske znanosti

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