Naslov
Giant, dissecting, high-pressure pulmonary artery aneurysm - case report of a 1-year natural course

Autori
Šmalcelj, Anton ; Brida, Vojtjeh ; Samaržija, Miroslav ; Matana, Ante ; Margetić, Eduard ; Drinković, Nikša

Izvornik
Texas Heart Institute journal (0730-2347) 32 (2005), 4; 589-594

Vrsta, podvrsta i kategorija rada
Radovi u časopisima, članak, stručni

Ključne riječi
aneurysm ; dissecting/diagnosis/etiology ; hypertension ; pulmonary/complications/therapy ; pulmonary artery/pathology ; sildenafil ; vasodilator agents/therapeutic use

Sažetak
We report the rare subchronic clinical course of a giant, dissecting pulmonary artery aneurysm in an oligosymptomatic middle-aged woman who had idiopathic pulmonary hypertension. Diagnosis was simple with the use of echocardiography and multislice computed tomography. Conversely, deciding on the treatment was difficult, because prominent surgeons declined to perform surgical repair of the aneurysm and recommended heart– lung transplantation. Therefore, we were forced to treat our patient medically. She survived for 1 year, including 8 months of treatment with sildenafil, and then died suddenly while awaiting transplantation. Our patient, who had a dissecting, high-pressure pulmonary artery aneurysm, had an unexpectedly stable and uneventful clinical course for 1 year, which, under more favorable circumstances, might have provided enough time for heart– lung transplantation to be performed.

Izvorni jezik
Engleski

Znanstvena područja
Kliničke medicinske znanosti

POVEZANOST RADA