Pregled bibliografske jedinice broj: 1092305
EULAR/PReS Online Course in Paediatric Rheumatology (chapter: Vasculitis)
EULAR/PReS Online Course in Paediatric Rheumatology (chapter: Vasculitis) / Martini, Alberto ; Hachulla, Eric (ur.)., 2020
CROSBI ID: 1092305 Za ispravke kontaktirajte CROSBI podršku putem web obrasca
Naslov
EULAR/PReS Online Course in Paediatric
Rheumatology (chapter: Vasculitis)
Autori
Jelusic, Marija ; Eleftheriou, Despina ; Brogan, Paul ; Ozen, Seza
Vrsta obrazovnog materijala
Udžbenik (visokoškolsko obrazovanje)
Izdavač
NA
Godina
2020
Stranica
NA
Ključne riječi
Vasculitis
Sažetak
Most of the primary vasculitic syndromes, apart from IgA vasculitis and Kawasaki disease, are rare in childhood, but are associated with significant morbidity and mortality. Classification criteria for childhood vasculitis have been developed, but should not be misused as diagnostic criteria. The cause of most vasculitides is unknown, although it is likely that a complex interaction between environmental factors such as infections and inherited host responses trigger the disease and determine the vasculitis phenotype. Monogenic forms of vasculitis are increasingly described. Treatment regimens continue to improve, with the use of different immunosuppressive medications and newer therapeutic approaches such as biological agents and development of more targeted therapies, although the evidence base remains limited in pediatric practice.
Izvorni jezik
Engleski
Znanstvena područja
Kliničke medicinske znanosti
POVEZANOST RADA
Projekti:
IP-2019-04-8822 - Histološki, klinički, laboratorijski i genski prediktori ishoda bolesnika s Henoch-Schönleinovom purpurom i nefritisom (PURPURAPREDICTORS) (Jelušić, Marija, HRZZ - 2019-04) ( CroRIS)
Ustanove:
Medicinski fakultet, Zagreb,
Klinički bolnički centar Zagreb
Profili:
Marija Jelušić
(autor)