Naslov
Porcelain aorta and peripheral arterial disease in a patient with Fahr disease

Autori
Cvjetko, Ivan ; Lubina, Zvonimir Ivan ; Pazur, Vedran

Izvornik
Journal of Vascular Surgery (0741-5214) 62 (2015), 4; 1073-1073

Vrsta, podvrsta i kategorija rada
Radovi u časopisima, članak, znanstveni

Ključne riječi
calcification, idiopathic, nonarteriosclerotic , cerebral vessels, aorta

Sažetak
Fahr disease is an idiopathic nonarteriosclerotic symmetrical calcification of cerebral vessels. This disease has been recognized as a histopathologic entity, and dozens of typical cases have been reported. Patients typically present with numerous neurologic and psychiatric symptoms.1 A 49-year-old woman, with no history of cardiovascular disease, was referred to our hospital due to intermittent claudication. She also complained of headache and occasional forgetfulness. Blood levels of glucose, lipids, iron, calcium, ferritin, alkaline phosphatase, thyroid hormones, and parathormone were within normal limits. A general workup quickly revealed heavy calcifications of blood vessels, mainly the aorta and the arteries arising from the aortic arch. Dense calcifications were seen on plain X-ray images (A). Multislice computed tomography imaging showed dense calcifications and narrowing of the complete aorta down to the common iliac arteries (B and C). Brain computed tomography imaging showed extensive bilateral and symmetrical parenchymal calcification mostly in the basal ganglia and nucleus dentate, characteristic for Fahr disease (D). Angiography and percutaneous transluminal angioplasty of the infrarenal aorta were performed through the common femoral artery. With additional walking exercise, the patient’s walking distance at the 1-year follow-up increased from 100 to 250 meters

Izvorni jezik
Engleski

Znanstvena područja
Kliničke medicinske znanosti

POVEZANOST RADA