Pregled bibliografske jedinice broj: 1045468
PHACES Syndrome with Intestinal Hemangiomatosis
PHACES Syndrome with Intestinal Hemangiomatosis // Acta dermatovenerologica Croatica, 27 (2019), 4; 265-269 (recenziran, članak, znanstveni)
CROSBI ID: 1045468 Za ispravke kontaktirajte CROSBI podršku putem web obrasca
Naslov
PHACES Syndrome with Intestinal Hemangiomatosis
Autori
Vrkić Boban, Ivona ; Lozić, Bernarda ; Stričević, Luka ; Čulo Čagalj, Ivana ; Skelin Glavaš, Ana ; Krželj, Vjekoslav
Izvornik
Acta dermatovenerologica Croatica (1330-027X) 27
(2019), 4;
265-269
Vrsta, podvrsta i kategorija rada
Radovi u časopisima, članak, znanstveni
Ključne riječi
PHACES syndrome ; neonate ; intestinal hemangiomatosis
Sažetak
We present a rare case of a neonate with PHACES syndrome (posterior fossa malformations, large facial hemangiomas, cerebral arterial anomalies, cardiovascular anomalies, eye anomalies and sternal clefting or supraumbilical raphe) and diffuse hemangiomatosis of the ileum, presenting with multiple intestinal perforations and peritonitis. The infant was successfully treated with propranolol and methylprednisolone as well as octreotide, tranexamic acid, and supportive therapy for massive intestinal bleeding.
Izvorni jezik
Engleski
Znanstvena područja
Kliničke medicinske znanosti
POVEZANOST RADA
Ustanove:
Medicinski fakultet, Split,
Sveučilište u Splitu Sveučilišni odjel zdravstvenih studija
Citiraj ovu publikaciju:
Časopis indeksira:
- Web of Science Core Collection (WoSCC)
- Science Citation Index Expanded (SCI-EXP)
- SCI-EXP, SSCI i/ili A&HCI
- Scopus
- MEDLINE