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Pregled bibliografske jedinice broj: 1045468

PHACES Syndrome with Intestinal Hemangiomatosis


Vrkić Boban, Ivona; Lozić, Bernarda; Stričević, Luka; Čulo Čagalj, Ivana; Skelin Glavaš, Ana; Krželj, Vjekoslav
PHACES Syndrome with Intestinal Hemangiomatosis // Acta dermatovenerologica Croatica, 27 (2019), 4; 265-269 (recenziran, članak, znanstveni)


CROSBI ID: 1045468 Za ispravke kontaktirajte CROSBI podršku putem web obrasca

Naslov
PHACES Syndrome with Intestinal Hemangiomatosis

Autori
Vrkić Boban, Ivona ; Lozić, Bernarda ; Stričević, Luka ; Čulo Čagalj, Ivana ; Skelin Glavaš, Ana ; Krželj, Vjekoslav

Izvornik
Acta dermatovenerologica Croatica (1330-027X) 27 (2019), 4; 265-269

Vrsta, podvrsta i kategorija rada
Radovi u časopisima, članak, znanstveni

Ključne riječi
PHACES syndrome ; neonate ; intestinal hemangiomatosis

Sažetak
We present a rare case of a neonate with PHACES syndrome (posterior fossa malformations, large facial hemangiomas, cerebral arterial anomalies, cardiovascular anomalies, eye anomalies and sternal clefting or supraumbilical raphe) and diffuse hemangiomatosis of the ileum, presenting with multiple intestinal perforations and peritonitis. The infant was successfully treated with propranolol and methylprednisolone as well as octreotide, tranexamic acid, and supportive therapy for massive intestinal bleeding.

Izvorni jezik
Engleski

Znanstvena područja
Kliničke medicinske znanosti



POVEZANOST RADA


Ustanove:
Medicinski fakultet, Split,
Sveučilište u Splitu Sveučilišni odjel zdravstvenih studija

Profili:

Avatar Url Vjekoslav Krželj (autor)

Avatar Url Bernarda Lozić (autor)

Poveznice na cjeloviti tekst rada:

hrcak.srce.hr pubmed.ncbi.nlm.nih.gov

Citiraj ovu publikaciju:

Vrkić Boban, Ivona; Lozić, Bernarda; Stričević, Luka; Čulo Čagalj, Ivana; Skelin Glavaš, Ana; Krželj, Vjekoslav
PHACES Syndrome with Intestinal Hemangiomatosis // Acta dermatovenerologica Croatica, 27 (2019), 4; 265-269 (recenziran, članak, znanstveni)
Vrkić Boban, I., Lozić, B., Stričević, L., Čulo Čagalj, I., Skelin Glavaš, A. & Krželj, V. (2019) PHACES Syndrome with Intestinal Hemangiomatosis. Acta dermatovenerologica Croatica, 27 (4), 265-269.
@article{article, author = {Vrki\'{c} Boban, Ivona and Lozi\'{c}, Bernarda and Stri\v{c}evi\'{c}, Luka and \v{C}ulo \v{C}agalj, Ivana and Skelin Glava\v{s}, Ana and Kr\v{z}elj, Vjekoslav}, year = {2019}, pages = {265-269}, keywords = {PHACES syndrome, neonate, intestinal hemangiomatosis}, journal = {Acta dermatovenerologica Croatica}, volume = {27}, number = {4}, issn = {1330-027X}, title = {PHACES Syndrome with Intestinal Hemangiomatosis}, keyword = {PHACES syndrome, neonate, intestinal hemangiomatosis} }
@article{article, author = {Vrki\'{c} Boban, Ivona and Lozi\'{c}, Bernarda and Stri\v{c}evi\'{c}, Luka and \v{C}ulo \v{C}agalj, Ivana and Skelin Glava\v{s}, Ana and Kr\v{z}elj, Vjekoslav}, year = {2019}, pages = {265-269}, keywords = {PHACES syndrome, neonate, intestinal hemangiomatosis}, journal = {Acta dermatovenerologica Croatica}, volume = {27}, number = {4}, issn = {1330-027X}, title = {PHACES Syndrome with Intestinal Hemangiomatosis}, keyword = {PHACES syndrome, neonate, intestinal hemangiomatosis} }

Časopis indeksira:


  • Web of Science Core Collection (WoSCC)
    • Science Citation Index Expanded (SCI-EXP)
    • SCI-EXP, SSCI i/ili A&HCI
  • Scopus
  • MEDLINE





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