Naslov
Case report of congenital cystic adenomatoid malformation type III with lethal outcome

Autori
Kulas, Tomislav ; Duic, Zeljko ; Reljica Kostic, Zlatka ; Zegarac, Zana ; Grizelj, Ruza ; Habek, Dubravko ; Hrgovic, Zlatko ; Marton, Ingrid ; Izetbegovic, Sebija

Izvornik
Medicinski arhiv (0350-199X) 64 (2010), 1; 55-59

Vrsta, podvrsta i kategorija rada
Radovi u časopisima, prikaz, stručni

Ključne riječi
congenital cystic adenomatoid malformation, prenatal ultrasound diagno- sis, therapy, outcome

Sažetak
We present a rare case of congenital cystic adenomatoid malformation (CCAM) type III (mycrocystic) in young, 19 years old primi- gravida. Diagnosis has been accomplished by ultrasound examination in 26th week of gestation. Hyperechogenic, mycrocystic mass was found in left pulmonary lobe with contra lateral displacement of mediastinum, hypoplasia of the right lung and extensive polyhydramnios. Prenatal therapy was based upon a serial of amniodrainage procedures and pharmacological inhibition of amni- otic fluid production and uterine activity. Spontaneous preterm labor occurred at 34 weeks of gestation. Diagnosis was confirmed postnatal. Infant was ventilated due to respiratory insufficiency and was operated at the age of 24 hours. Lethal outcome occurred during the second day due to heavy respira- tory insufficiency provoked by pulmonary hypoplasia. We discuss about types of a disease, prenatal diagnostic and therapeutic possibilities and pregnancy outcome.

Izvorni jezik
Engleski

Znanstvena područja
Kliničke medicinske znanosti

POVEZANOST RADA