engleski

Primary malignant fibrous histiocytoma of the heart with skeletal muscles metastases

Malignant fibrous histiocytoma is extremely rare primary malignant tumor of the heart. It is usually diagnosed when it is locally aggressive or has already metastasized. The prognosis is poor despite surgery and the availability of chemotherapeutic regimens with the average survival time of one year. We report a case of recurrent left atrial malignant fibrous histiocytoma initially misdiagnosed as atrial myxoma. After repeated surgical resection no signs of extracardiac extension were found, adjuvant chemotherapy was started and patient was scheduled for cardiac transplantation. Unfortunately, while we were waiting for organ distal metastasis in the plantar surface of her right foot occurred and patient had to be removed from transplantation list. Despite adjuvant chemotherapy, 18 months after initial diagnosis definitive tumor relapse in left atrium was diagnosed. This is the 48th case of primary cardiac fibrous malignant histiocytoma reported in literature.

Echocardiography; heart; malignant fibrous histiocytoma; metastases

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