Familial antiphospholipid syndrome presenting as bivessel arterial occlusion in a 17-year old girl (CROSBI ID 211648)
Prilog u časopisu | kratko priopćenje | međunarodna recenzija
Podaci o odgovornosti
Jelušić, Marija ; Starčević, Katarina ; Dobrota, Savko ; Banfić. Ljiljana ; Potočki, kristina ; Anić, Branimir
engleski
Familial antiphospholipid syndrome presenting as bivessel arterial occlusion in a 17-year old girl
This article presents a case of a 17-year-old girl with primary antiphospholipid syndrome developing subacute signs of hand and leg ischaemia caused by radiologically verified radial and popliteal artery occlusion. She is successfully treated with a thrombolytic agent (alteplase) and recovers completely. Her laboratory results came positive for all three subtypes of antiphospholipid antibodies. This kind of antiphospholipid syndrome presentation is a very rare entity in itself. Shortly afterwards her mother is diagnosed with primary antiphospholipid syndrome as well. A familial form of antiphospholipid syndrome is suspected. Combination of a familial antiphospholipid syndrome presenting as bivessel arterial thrombosis is a unique case, to the best of our knowledge, never described in the literature before
antiphospholipid syndrome; familial
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Podaci o izdanju
Povezanost rada
Kliničke medicinske znanosti