engleski

A severe iron deficiency anemia in an 18-year old boy with idiopathic pulmonary hemosiderosis.

Idiopathic pulmonary hemosiderosis is a rare condition of unknown etiology, without established incidence or prevalence, characterised with reccurent episodes of diffuse alveolar bleeding and subsequent iron deficiency anemia. It is found mostly in children, clinical course varies greatly, not recognized and not treated often results in a fatal episode of respiratory hemorrhage. Mortality is considered high. Diagnosis is grounded on evident diffuse intrapulmonary bleeding, secondary sideropenic anemia and finding of numerous erythrocites and siderophages in sputum/bronchoalveolar lavage. Next step is obligatory exclusion of every other known couse of diffuse alveolar hemorrhage mainly with laboratory and immunologic tests whose results should be confirmed and concluded with a finding of lung biopsy. Our case-report depicts a patient of an adolescent age who presented himself with a severe sideropenic anemia, with no cough at the time or hemoptysis ever. His diagnosis remained unknown for several months. All obtained diagnostic procedures considered as standard led us to a dead-end. Later, only after a massive life-threatening hemoptoe we started considering idiopathic pulmonary hemosiderosis as an underlying condition. Bronchoalveolar lavage and lung-biopsy resolved our query.

Idiopathic pulmonary hemosiderosis; anemia

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