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izvor podataka: crosbi

Sepsis as an Unusual event in Dyskeratosis Follicularis (CROSBI ID 90612)

Prilog u časopisu | izvorni znanstveni rad | međunarodna recenzija

Milavec-Puretić, Višnja ; Lipozenčić, Jasna ; Šustić, Nela ; Pećina-Šlaus, Nives Sepsis as an Unusual event in Dyskeratosis Follicularis // Croatian medical journal, 42 (2001), 1; 64-66-x

Podaci o odgovornosti

Milavec-Puretić, Višnja ; Lipozenčić, Jasna ; Šustić, Nela ; Pećina-Šlaus, Nives

engleski

Sepsis as an Unusual event in Dyskeratosis Follicularis

Dyskeratosis follicularis is a genetic disorder characterized by pathogenetic changes of keatinization. We report on a severe case of the disease with an unusual manifestation involving Staphylococcal sepsis. The patient was treated with infusions and oral antibiotics and retinoids. Topically, antiseptics and keratolytic ointments and creams were given to promote epithelisation. His condition improved dramatically after 14 days of treatment. All erosions of the trunk, extremities, neck, and head had epithelised. We suspect that the sepsis was triggered by extreme sun exposure and neglect of care on genetically susceptible sites.

keratosis follicularis; Darier's Disease; Staphylococcal sepsis

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Podaci o izdanju

42 (1)

2001.

64-66-x

objavljeno

0353-9504

Povezanost rada

Kliničke medicinske znanosti

Indeksiranost