engleski

Myocardial Noncompaction in a Newborn – Case Report,

Myocardial noncompaction is rare condition characterized by an altered structure of the myocardial wall due to incomplete myocardial ontogenesis. Clinical symptoms may appear at any age and include heart failure, arrhythmias and cardioembolic events. We present a newborn with myocardial noncompaction and no congenital heart malformation. Our patient was born from uncomplicated pregnancy. Shortly after delivery he developed symptoms of the heart failure and noncompaction was diagnosed according to the criteria suggested by Jenni et al. and by Sulafa and al. prospective study. The finding of multiple trabeculations and recesses on cross-sectional imaging, with the appearance of distinct compacted and noncompacted myocardial layers, low scale colour flow mapping the delineating the continuity of intertrabecular recesses with the ventricular cavity and a ratio of 1.9:1 of the thicknesses of the noncompacted to compacted layers and noncompaction myocardial structure was noticed. We started treatment with diuretics, ACE inhibitors, low doses of digitalis, calcium inhibitors and antiagregation therapy. His general condition improved but his weight increased slowly. Psychomotor development is mainly within normal limits. Myocardial noncompaction is mostly noticeable at the apicoseptal segment. Ejection fraction maintained at 45-50% (fractional shortening 23- 28%), but with depressed diastolic function and left atrium enlargement, pathological mitral valve motion, venooclusive pulmonary hypertension and mild stenosis of the isthmus of the aorta. There were no arrhythmias during therapy and no criteria for Roifman syndrome. He is followed for 7.5 months. We also present the first echocardiographic record of the reptile myocardium which philogenetic structure probably reflex human noncompaction myocardium

Myocardial noncompaction

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