engleski

Prosthetic rehabilitation of a patient with cleidocranial dysostosis

Cleidocranial dysostosis (ccd) is characterised by a triad: clavicular aplasia, delayed ossification of the fontanelles and a sutures of the vault of the skull and hereditary transmission. Also, it concerns both teeth and jaw and is characterized by supernumerary teeth, delayed resorption of deciduous teeth and eruption of permanent teeth, tooth impaction and eventually follicular cysts. Developmental deformities of the permanent dentition are of primary concern in the prosthetic treatment of patients suffering from ccd. A patient 26 years of age with ccd was examined at our Prosthetic Department. Previously, he was chirurgically treated. Deciduous teeth were extracted, and corticotomy was performed in order to enable eruption of permanent teeth. Firstly, temporary removable prostheses were made for evaluation of the patient's ability to adapt to the newly determined vertical dimension of occlusion and to stimulate the eruption of permanent teeth. The patient wore the temporary removable partial prostheses for one year. Because patient was comfortable with the newly determined vertical dimension, it was decided that the final restoration would be constructed accordingly. Unfortunately no eruption of embedded teeth was obtained. Telescopic crowns, coping with intraradicular retention and Dalla Bona stud attachment, and metal-base partial dentures were designed resulting in satisfactory function and esthetics. Prosthetic treatment of the oral condition is very important, not only to restore function and esthetics but also to resolve the problems of appearance associated with this disease.

cleidocranial dysostosis; prosthetic rehabilitation; prosthetic dentistry

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