engleski

Ochronosis of the aortic valve and aorta

A 64-year-old patient with unknown alcaptonuria with severe aortic stenosis and ischemic heart disease was admitted in our instituion for elective surgery. The patient underwent surgery, aortic valve replacement using 25 mm ATS Medical, INC aortic valve and single venous aortocoronary artery bypass grafting for a right coronary artery. Aortotomy revealed a tipically ochronotic pigmentation of a severe calcified aortic valve and the aortic intima. Diagnosis of alcaptonuria was confirmed with evidence of homogentisic acid in urine and with histopathological analysis.

Ochronosis; aortic valve

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