Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report (CROSBI ID 310066)
Prilog u časopisu | stručni rad | međunarodna recenzija
Podaci o odgovornosti
Grizelj, Ruža ; Sindičić Dessardo, Nada ; Bulić, Krešimir ; Luetić, Tomislav ; Mikulić, Danko ; Antabak, Anko ; Sjekavica, Ivica ; Alduk, Ana Marija ; Konosić, Sanja ; Režek Tomašić, Karolina ; Ćaleta, Tomislav ; Pleško, Sanja ; Šarić, Dalibor ; Vuković, Jurica
engleski
Successful separation of xypho-omphalopagus conjoined twins with extrauterine twin-twin transfusion syndrome: a case report
Conjoined twining is a rare medical phenomenon, with an overall prevalence of 1.47 per 100000 births. This report describes a successful separation of xypho-omphalopa- gus conjoined twins complicated by unbalanced blood shunting through the porto- systemic anastomoses within the shared liver parenchyma. Significant extrauterine twin- twin transfusion syndrome caused by unbalanced shunt- ing is an extremely rare, and probably under- recognized, hemodynamic complication in conjoined twins necessi- tating urgent separation. Progressive deterioration with a poor outcome can be prevented if the condition is recog- nized in a timely manner.
conjoined twins ; extrauterine twin-twin transfusion syndrome
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Podaci o izdanju
60 (4)
2019.
301-308
objavljeno
0353-9504
1332-8166
10.3325/cmj.2019.60.301
Povezanost rada
Kliničke medicinske znanosti