engleski

A newborn with high-output cardiac failure due to a large vein of Galen malformation

Neonatal heart failure in newborns is often caused by asphyxial cardiomyopathy, left-sided obstructive lesions, large mixing cardiac defects and myocarditis. The most frequent haemodynamically significant extracardiac arterio– venous shunt found in newborns is a vein of Galen malformation. However, it is not a frequent cause of severe cardiac failure in infancy. Effective treatment has not yet been found. We report on a patient with a large vein of Galen malformation who presented with high-output cardiac failure, pulmonary artery hypertension and respiratory distress soon after birth. During an emergency cardiac catheterisation, we diagnosed a large vein of Galen malformation. The cardiac status was improved after partial embolisation. Nine months later the echocardiographic finding was normal and further therapy was discontinued. Unfortunately, as in similar cases, hypertensive hydrocephalus developed. A ventriculoperitoneal shunt was placed but there were major neurodevelopmental delays.

Neonatal heart failure ; asphyxial cardiomyopathy

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