Malignant Perivascular Epitheloid Cell Tumor with an Unusual Immunophenotype in a Ten-Year-Old Child (CROSBI ID 274612)
Prilog u časopisu | izvorni znanstveni rad | međunarodna recenzija
Podaci o odgovornosti
Jonjic, Nives ; Roganovic, Jelena ; Glavan, Nedeljka ; Hadzisejdic, Ita ; Seili-Bekafigo, Irena
engleski
Malignant Perivascular Epitheloid Cell Tumor with an Unusual Immunophenotype in a Ten-Year-Old Child
Introduction: Perivascular epitheloid cell tumors (PEComa) represent a group of usually benign mesenchymal neoplasms. Malignant variants are usually found only in adults.Case: We present a 10-year-old girl with infraclavicular malignant PEComa, negative for HMB-45 and Melan A but focally positive for MITF.Conclusion: To the best of our knowledge, no malignant variant of PEComa has been described in soft tissue in a child. Generally, PEComas are immunoreactive for HMB-45 and/or Melan A while our case was negative for both. Further studies are necessary to elucidate the significance of this immunohistochemical finding.
PEComa ; malignant perivascular epitheloid cell tumor ; pediatric PEComa
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Podaci o izdanju
38 (6)
2019.
503-510
objavljeno
1551-3815
10.1080/15513815.2019.1604923
Povezanost rada
Kliničke medicinske znanosti