PHACES Syndrome with Intestinal Hemangiomatosis (CROSBI ID 274151)
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Podaci o odgovornosti
Vrkić Boban, Ivona ; Lozić, Bernarda ; Stričević, Luka ; Čulo Čagalj, Ivana ; Skelin Glavaš, Ana ; Krželj, Vjekoslav
engleski
PHACES Syndrome with Intestinal Hemangiomatosis
We present a rare case of a neonate with PHACES syndrome (posterior fossa malformations, large facial hemangiomas, cerebral arterial anomalies, cardiovascular anomalies, eye anomalies and sternal clefting or supraumbilical raphe) and diffuse hemangiomatosis of the ileum, presenting with multiple intestinal perforations and peritonitis. The infant was successfully treated with propranolol and methylprednisolone as well as octreotide, tranexamic acid, and supportive therapy for massive intestinal bleeding.
PHACES syndrome ; neonate ; intestinal hemangiomatosis
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Podaci o izdanju
Povezanost rada
Kliničke medicinske znanosti